PROGRESSIVE FIBROSING-INTERSTITIAL LUNG DISEASE (PF-ILD) BEhaves IN A CLINICALLY SIMILAR WAY to IPF1

See the connection
Like IPF, the disease course of PF-ILD is characterized by1:
Diagram Disease
Similar to IPF, loss of lung function can be rapid in some patients WITH PF-ILD2,4
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Diagram Disease
Many patients with PF-ILD follow a similar survival pattern to IPF3-13
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Diagram Disease
1 out of 3 SSc-related deaths was due to ILD14
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DLCO, diffusing capacity for carbon monoxide; FVC, forced vital capacity; HP, hypersensitivity pneumonitis; IIP, idiopathic interstitial pneumonia; IPF, idiopathic pulmonary fibrosis; RA-ILD, rheumatoid arthritis-associated interstitial lung disease; SSc-ILD, systemic sclerosis-associated interstitial lung disease.

References: 1. Flaherty KR et al. BMJ Open Resp Res. 2017;4(1):1-7. 2. Zappala CJ et al. Eur Respir J. 2010;35(4):830-835. 3. Gimenez A et al. Thorax. 2018;73(4):391-392. 4. Ryerson CJ et al. Eur Respir J. 2013;42(3):750-757. 5. Hyldgaard C et al. Respirology. 2017;22(3):494-500. 6. Wells AU et al. Am J Respir Crit Care Med. 1994;149(6):1583-1590. 7. Mapel DW et al. Thorax. 1998;53(6):469-476. 8. Hubbard R et al. Chest. 1998;113(2):396-400. 9. Goh NSL et al. Am J Respir Crit Care Med. 2008;177(11):1248-1254. 10. Moore OA et al. Rheumatology. 2013;52(1):155-160. 11. Kim EJ et al. Eur Respir J. 2010;35(6):1322-1328. 12. Bongartz T et al. Arthritis Rheum. 2010;62(6):1583-1591. 13. Vourlekis JS et al. Am J Med. 2004;15(10):662-668. 14. Tyndall AJ et al. Ann Rheum Dis. 2010;69(10):1809-1815.